Fig. (1)
Clinical pedigree of the family. Family pedigree showing members with dominant DEB
Notes: Affected individuals: stripe; death: slash
Patient 1 (2.2) had extensive skin blistering and dystrophic nails. The lesions healed with scar formation.
Patient 2 (3.6) & patient 3 (3.12) had extensive skin blistering, erosions, and dystrophic nails.
Patient 4 (4.1) had skin blisters, erosions, and dystrophic nails with mucous involvement. The lesions healed with scar formation.
Patient 5 (4.4) had minor blistering on area with friction and erosions, with nail involvement. Lesions healed with minor scar formation.