Table 1: Examples of Primary (Idiopathic) and Secondary Fibrotic Disorders with Multiple/Single Organ Presentation

Primary Secondary
Systemic
Systemic sclerosis Graft versus host disease
Drug-induced nephrogenic systemic fibrosis
Sarcoidosis Secondary amyloidosis
Amyloidosis Post-radiation
Toxic environmental exposure
Storage disorders (hemochromatosis, glycogenosis, Gaucher’s disease, etc)
Lungs
Idiopathic pulmonary fibrosis Pneumoconiosis
Histiocytosis X Infectious pneumonitis
Cryptogenic organizing pneumonia Tuberculosis
Hypersensitive pneumonitis
Inherited disorders
Autoimmune diseases
Transplant rejection
Drug-induced
Post-radiation
Sarcoidosis
Amyloidosis
Heart
Idiopathic restrictive cardiomyopathy Coronary artery disease/myocardial infarction
Pressure-overload heart (long standing arterial hypertension, valvular disease)
Infectious myocarditis
Autoimmune diseases
Transplant rejection
Familial hypertrophic cardiomyopathy
Arrhythmogenic right ventricular cardiomyopathy
Drug-induced
Post-radiation
Sarcoidosis
Amyloidosis
Kidney
Idiopathic nephrotic syndrome Diabetic glomerulosclerosis
Idiopathic membranoproliferative glomerulonephritis Hypertensive nephrosclerosis
Autoimmune glomerular diseases
Drug-induced
Post-radiation
Amyloidosis
Transplant rejection
Liver
Primary biliary cirrhosis Chronic viral hepatitis
Primary sclerosing cholangitis Schistosomiasis
Alcoholic liver disease
Nonalcoholic fatty liver disease
Drug-induced
Toxic environmental exposure
Inherited metabolic disorders
Autoimmune hepatitis
Intestinal bypass