Table 2.: Primary reason for seeking medical attention in 25 patients of pSS with RTA.

Clinical Manifestations Number of
General systemic
Fatigue* 1
Ocular symptoms
Dry eyes* 1
Corneal opacity 1
 Acute onset paralysis 7
Proximal muscle weakness* 1
 Referred as RTA* 1
Musculoskeletal / Rheumatological / autoimmune disorders
Multiple fractures* 1
Polyarthralgia * 1
Polyarthritis 2
Referred as SLE 1
Referred as SjÖgren with MGUS 1
Asymptomatic ANA positivity* 1
Asymptomatic mother of baby with neonatal lupus 1
Thrombocytopenia 1
Deranged LFT* 1
Parotidomegaly 1
Irregular cycles with short stature 1

* Asterix marked patients (n=9) also had past History of hypokalemic paralysis, but not as their presenting feature. Along with the 7 patients who presented with this complication, therefore a total of 16 patients with hypokalemic paralysis are included in this series as mentioned in the text
RTA Renal Tubular Acidosis; pSS Primary Sjögren Syndrome; ANA Anti-nuclear Antibody; MGUS Monoclonal Gammopathy of Undetermined Significance; AIHA Autoimmune haemolytic anemia; LFT Liver Function Test.