| Age/Gender | Associated Findings | Duration of IVIG Therapy | Therapy Prior to IVIG | Therapy After IVIG | Response# |
|---|---|---|---|---|---|
| 45 Female [7] |
ILD | 5 day course (400 mg/kg/day) total 2gm/kg Two Courses, one month apart |
PSL 60/day CSA 250/day |
PSL taper (60 to 20 - 4 months) CSA 250/day |
Survived (Condition not otherwise described) |
| 72 Male [7] |
ILD | 5 day course (400 mg/kg/day) total 2gm/kg One Course |
MPD* PSL 60/day CSA* CYC* |
PSL* CSA* Polymyxin B Hemoperfusion |
Died (46 days after onset of illness) |
| 75 Female [7] |
ILD | 5 day course (400 mg/kg/day) total 2gm/kg One Course |
MPD* PSL 50/day CSA* |
PSL* CSA* CYC* |
Died (47 days after onset of illness) |
| 55 Female [7] |
ILD | 5 day course (400 mg/kg/day) total 2gm/kg One Course |
MPD* PSL 50/day CSA* |
PSL* CSA* CYC* |
Died (29 days after onset of illness) |
| 24 Male [7]¶ |
ILD | 5 day course (400 mg/kg/day) total 2gm/kg Two Courses, one month apart |
MPD 3g PSL 60/day |
CSA 150 mg/day PSL taper (60 to 10 mg) |
Survival, with resolution of pulmonary and cutaneous findings |
| 55 Female [8] |
Calcinosis Cutis | 5 day course (400 mg/kg/day) total 2gm/kg Five Courses one month apart, then one course yearly for 5 years |
Pred 60/day HCQ 400/day CLQ 250/day MTX 7.5/week AZA 100/day CSA 200/day MMF 1500/day |
No immunomodulatory therapy | Complete resolution |
| 54 Male [9] |
ILD | 5 day course (400 mg/kg/day) total 2gm/kg One Course |
PRED taper (30 mg over 12 days) MPD 3 g PRED 75/day |
PRED 75/day | Died |
| 61 Female [10]§ |
None Noted | 2 day course (1gm/kg/day) Total 2gm/kg 7 courses, one month apart |
HCQ* PRED 40/day |
No immunomodulatory therapy | Complete resolution |
| 29 Female [10] |
None Noted | 2 day course (1gm/kg/day) Total 2gm/kg 28 courses, one month apart |
HCQ* MMF* MTX* |
HCQ* | Complete Resolution |
| 36 Female [10] |
None Noted | 2 day course (1gm/kg/day) Total 2gm/kg 22 courses, one month apart |
HCQ* MTX* |
No immunomodulatory therapy | Complete Resolution |
| 22 Female [10]§ |
None Noted | 2 day course (1gm/kg/day) Total 2gm/kg 6 courses, one month apart |
HCQ* | HCQ* | Complete Resolution |
| 53 Female [10]§ |
None Noted | 2 day course (1gm/kg/day) Total 2gm/kg 4 courses, one month apart |
HCQ* MTX* |
No immunomodulatory Therapy | Complete Resolution |
| 93 Female [10] |
None Noted | 2 day course (1gm/kg/day) Total 2gm/kg 4 courses, one month apart |
HCQ* PRED 10/daily |
No immunomodulatory Therapy | >75% resolution |
| 56 Female [10] |
None Noted | 2 day course (1gm/kg/day) Total 2gm/kg 11 courses, one month apart |
HCQ* MMF* MTX* |
HCQ* (summer months only) |
>75% resolution |
| 87 Female [10] |
None Noted | 2 day course (1gm/kg/day) Total 2gm/kg 9 courses, one month apart |
HCQ* | None | <75% resolution |
| 58 Male [10] |
None Noted | 2 day course (1gm/kg/day) Total 2gm/kg 7 courses, one month apart |
HCQ* THAL* MTX* PRED 40/day |
PRED 20/day | <75% resolution |