Table 2: Pathological findings including immunofluorescence and electron microscopy findings. staining intensity on five-grade scale of 0 - 3+; 0, negative; <1+, spare; 1+, weak; 2+, moderate; 3+, strong
Patient |
Immunofluorescence |
Electron Microscopy |
|
PLA2R |
IgG |
IgA |
IgM |
C3 |
C4 |
C1q |
IgG Subclass |
Lesions with |
Ehrenreich-Churg |
|
|
|
|
|
|
|
|
IgG1 |
IgG2 |
IgG3 |
IgG4 |
IgG Deposits |
stage |
1 |
- |
2+ |
0 |
<1+ |
0 |
0 |
0 |
0 |
0 |
1+ |
0 |
global |
stage 1/2 |
2 |
- |
1+ |
1+ |
0 |
<1+ |
1+ |
0 |
0 |
0 |
0 |
0 |
global |
stage 1 |
3 |
- |
3+ |
<1+ |
1+ |
1+ |
<1+ |
1+ |
0 |
0 |
2+ |
1+ |
global |
stage 1 |
4 |
- |
2+ |
0 |
0 |
<1+ |
0 |
0 |
0 |
0 |
0 |
0 |
NA |
stage 1 |
5 |
- |
2+ |
0 |
1+ |
2+ |
0 |
0 |
0 |
0 |
2+ |
0 |
NA |
stage 1/2 |
6 |
- |
2+ |
0 |
0 |
0 |
0 |
1+ |
0 |
0 |
1+ |
0 |
segmental |
stage 2 |
7 |
- |
2+ |
0 |
0 |
<1+ |
0 |
0 |
0 |
0 |
1+ |
0 |
global |
stage 1 |
8 |
+ |
2+ |
0 |
0 |
1+ |
0 |
0 |
1+ |
0 |
<1+ |
1+ |
global |
stage 1 |
9 |
- |
2+ |
1+ |
0 |
0 |
0 |
2+ |
0 |
0 |
1+ |
0 |
segmental |
stage 2 |
10 |
- |
3+ |
0 |
0 |
<1+ |
3+ |
0 |
<1+ |
0 |
0 |
1+ |
global |
stage 2 |
11 |
- |
3+ |
1+ |
0 |
2 |
3+ |
0 |
1+ |
1+ |
0 |
3+ |
global |
stage 1 |
PLA2R: Phospholipase A2 receptor, NA: data not available, Ig: Immunoglobulin, C: Complement