Table 2: Genetic disorders of the glomerular basement membrane disorders.

Gene Protein Inheritance Onset Comments
α-5 chain α-5 chain X-linked Early childhood Alport syndrome - ESRD at 2-4 decade, Deafness
Heterozygous α-3 or α-4 mutation α-3 or α-4 chain AD Early childhood Thine basement membrane disease -Familial hematuria
Homozygous α-3 or α-4 mutation α-3 or α-4 AR Early childhood Alport syndrome - ESRD at adolescence, deafness
LAMB2 Laminin 2 AR Infancy Pierson syndrome - Eye disease, MR
LMX1B LMX1B AD Variable Nail-Patella syndrome - Dysplastic nails and patellae, variable degree of renal involvement
ITGA3 Integrin α3 subunit AR Infancy Kidney disease, lung disease, epidermolysis bullosa